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Table 3: Number of Cases, Percent and
Age-Specific Incidence Rate* (ASIR) of First Primary Central Nervous System
Tumors among Children, Adolescents and Teens by Diagnositic Group, Age Group
and Tumor Behavior, California, 2001-2005 |
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< 5 years |
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5-9 years |
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Malignant |
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Benign |
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Uncertain |
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Total |
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Malignant |
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Benign |
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Uncertain |
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Total |
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Diagnostic
Groups |
|
n |
% |
ASIR |
95% CI |
|
n |
% |
ASIR |
95% CI |
|
n |
% |
|
n |
% |
|
n |
% |
ASIR |
95% CI |
|
n |
% |
ASIR |
95% CI |
|
n |
% |
|
n |
% |
|
IIIA Ependymomas & Choroid Plexus Tumor |
|
74 |
21.8% |
|
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|
21 |
13.6% |
0.2 |
(0.1,
0.2) |
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|
99 |
18.1% |
|
28 |
9.4% |
0.2 |
(0.1, 0.3) |
|
11 |
7.4% |
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|
6 |
9.2% |
|
45 |
8.8% |
|
IIIB Astrocytomas |
|
67 |
19.8% |
0.8 |
(0.6,
0.9) |
|
119 |
77.3% |
0.9 |
(0.8,1.1) |
|
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|
189 |
34.6% |
|
72 |
24.2% |
1.0 |
(0.9, 1.2) |
|
102 |
68.9% |
0.8 |
(0.6,
0.9) |
|
8 |
12.3% |
|
182 |
35.7% |
|
IIIC1 Medulloblastomas |
|
64 |
18.9% |
0.5 |
(0.4,
0.6) |
|
0 |
0.0% |
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0 |
0.0% |
|
64 |
11.7% |
|
68 |
22.9% |
0.5 |
(0.4, 0.7) |
|
0 |
0.0% |
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0 |
0.0% |
|
68 |
13.3% |
|
IIIC2 PNET |
|
47 |
13.9% |
0.4 |
(0.3,
0.5) |
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0 |
0.0% |
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0 |
0.0% |
|
47 |
8.6% |
|
29 |
9.8% |
0.2 |
(0.1, 0.3) |
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0 |
0.0% |
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0 |
0.0% |
|
29 |
5.7% |
|
IIIC9 Other Intracranial & Intraspinal |
|
18 |
5.3% |
0.1 |
(0.1,
0.2) |
|
0 |
0.0% |
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|
0 |
0.0% |
|
18 |
3.3% |
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0 |
0.0% |
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0 |
0.0% |
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IIID Other Gliomas |
|
40 |
11.8% |
0.4 |
(0.3,
0.5) |
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0 |
0.0% |
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0 |
0.0% |
|
40 |
7.3% |
|
73 |
24.6% |
0.6 |
(0.5, 0.8) |
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0 |
0.0% |
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0 |
0.0% |
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73 |
14.3% |
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IIIE Other Specified Intracranial & Intraspinal |
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36 |
66.7% |
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43 |
7.9% |
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22 |
14.9% |
0.2 |
(0.1,
0.3) |
|
46 |
70.8% |
|
71 |
13.9% |
|
XA Intracranial & Intraspinal Germ Cell |
|
8 |
2.4% |
|
|
|
5 |
3.2% |
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|
|
0 |
0.0% |
|
13 |
2.4% |
|
13 |
4.4% |
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|
|
|
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|
0 |
0.0% |
|
14 |
2.7% |
|
Z Other |
|
17 |
5.0% |
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|
6 |
3.9% |
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|
11 |
20.4% |
|
34 |
6.2% |
|
9 |
3.0% |
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|
12 |
8.1% |
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|
5 |
7.7% |
|
26 |
5.1% |
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Total |
|
339 |
100.0% |
2.6 |
(2.4,
2.9) |
|
154 |
100.0% |
1.2 |
(1.0,
1.4) |
|
54 |
100.0% |
|
547 |
100.0% |
|
297 |
100.0% |
2.3 |
(2.0, 2.5) |
|
148 |
100.0% |
1.1 |
(1.0,
1.3) |
|
65 |
100.0% |
|
510 |
100.0% |
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10-14 years |
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15-19 years |
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IIIA Ependymomas & Choroid Plexus Tumor |
|
23 |
9.0% |
0.2 |
(0.1,
0.3) |
|
5 |
3.1% |
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|
12 |
15.8% |
|
40 |
8.1% |
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21 |
9.4% |
0.2 |
(0.1, 0.2) |
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12 |
13.5% |
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37 |
6.8% |
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IIIB Astrocytomas |
|
66 |
25.9% |
0.7 |
(0.6,
0.9) |
|
89 |
55.6% |
0.7 |
(0.5,
0.8) |
|
7 |
9.2% |
|
162 |
33.0% |
|
71 |
31.8% |
0.6 |
(0.5, 0.8) |
|
61 |
25.8% |
0.5 |
(0.4,
0.6) |
|
5 |
5.6% |
|
137 |
25.0% |
|
IIIC1 Medulloblastomas |
|
28 |
11.0% |
0.2 |
(0.1,
0.3) |
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0 |
0.0% |
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0 |
0.0% |
|
28 |
5.7% |
|
23 |
10.3% |
0.2 |
(0.1, 0.3) |
|
0 |
0.0% |
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0 |
0.0% |
|
23 |
4.2% |
|
IIIC2 PNET |
|
17 |
6.7% |
0.1 |
(0.1,
0.2) |
|
0 |
0.0% |
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|
0 |
0.0% |
|
17 |
3.5% |
|
11 |
4.9% |
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0 |
0.0% |
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0 |
0.0% |
|
11 |
2.0% |
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IIIC9 Other Intracranial & Intraspinal |
|
0 |
0.0% |
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0 |
0.0% |
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0 |
0.0% |
|
0 |
0.0% |
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0 |
0.0% |
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0 |
0.0% |
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0 |
0.0% |
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0 |
0.0% |
|
IIID Other Gliomas |
|
51 |
20.0% |
0.4 |
(0.3,
0.5) |
|
0 |
0.0% |
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|
0 |
0.0% |
|
51 |
10.4% |
|
35 |
15.7% |
0.3 |
(0.2, 0.4) |
|
0 |
0.0% |
|
|
|
0 |
0.0% |
|
35 |
6.4% |
|
IIIE Other Specified Intracranial &
Intraspinal |
|
|
|
|
|
|
41 |
25.6% |
0.3 |
(0.2,
0.4) |
|
46 |
60.5% |
|
91 |
18.5% |
|
6 |
2.7% |
|
|
|
138 |
58.5% |
1.1 |
(0.9,
1.3) |
|
56 |
62.9% |
|
200 |
36.5% |
|
XA Intracranial & Intraspinal Germ Cell |
|
59 |
23.1% |
0.4 |
(0.3,
0.6) |
|
|
|
|
|
|
0 |
0.0% |
|
62 |
12.6% |
|
43 |
19.3% |
0.3 |
(0.2, 0.4) |
|
|
|
|
|
|
0 |
0.0% |
|
45 |
8.2% |
|
Z Other |
|
7 |
2.7% |
|
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|
22 |
13.8% |
|
|
|
11 |
14.5% |
|
40 |
8.1% |
|
13 |
5.8% |
|
|
|
31 |
13.1% |
|
|
|
16 |
18.0% |
|
60 |
10.9% |
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Total |
|
255 |
100.0% |
1.9 |
(1.6,
2.1) |
|
160 |
100.0% |
1.2 |
(1.0,
1.4) |
|
76 |
100.0% |
|
491 |
100.0% |
|
223 |
100.0% |
1.7 |
(1.5, 2.0) |
|
236 |
100.0% |
1.8 |
(1.6,
2.1) |
|
89 |
100.0% |
|
548 |
100.0% |
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*
Age-specific incidence rates are per 100,000 population. Rates are standardized to the 2000 US
population. |
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PNET =
Primitive Neuroectodermal Tumors |
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Shaded
cells = rates could not be calculated if number of cases were less than 15
and/or the underlying population was less than 100,000. |
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